Familial Adenomatous Polyposis (FAP)
- Autosomal Dominant
- Mutation on Chromosome 5
- APC Tumor Suppressor Gene Mutation
- Overexpression of β-catenin
- Two-Hit Hypothesis
- Postpubertal Appearance of Thousands of Polyps
- Always Involves Rectum
- Pancolonic
- Hepatoblastoma
- Most Patients Develop Colorectal Carcinoma (CRC) by 40 years of age
- Prophylactic Colectomy