Right to Left Heart Shunts
- The 5 Ts
- Truncus Arteriosus
- Transposition of the Great Vessels
- Tricuspid Atresia
- Tetralogy of Fallot
- Total Anomalous Pulmonary Venous Return (TAPVR)
- Cyanosis at Birth
- May Require PDA
Left-to-Right Heart Shunts
- The 3 Ds
- Ventricular Septal Defect (VSD)
- Atrial Septal Defect (ASD)
- PDA
- Later Cyanosis
- Clubbing
- Eisenmenger's Syndrome
Tetralogy of Fallot (TOF)
- Blue Baby Syndrome
- PROVe Acronym
- Pulmonary Infundibular Stenosis
- Right Ventricular Hypertrophy
- Overriding Aorta
- Ventricular Septal Defect (VSD)
- Boot-Shaped Heart
- Squatting for Tet Spells
- Surgery
Persistent Truncus Arteriosus
- Common Arterial Trunk
- Single Trunk Emerges from Both Ventricles
- Cyanosis
- Pulmonary Congestion
- Heart Failure
- Single S2 Sound
- Echocardiogram
- Chest X-ray
- Early Surgical Correction
- Avoids Pulmonary Hypertension
Atrial Septal Defect (ASD)
- Hole in Septum between the Atria
- Often Asymptomatic
- Wide and Fixed Split S2
- Cyanosis and Dyspnea
- Easily Fatigued
- Chest X-ray shows Increased Pulmonary Vascular Markings
- Echocardiogram
- Surgery if CHF as Child
- Antibiotic Prophylaxis
- Most Close Spontaneously
Ventricular Septal Defect (VSD)
- Opening at Intraventricular Septum
- Most Common Congenital Heart lesion
- High-pitched Holosystolic Murmer (over left sternal border)
- Dyspnea and Respiratory Distress
- Loud Pulmonic S2
- Echocardiogram
- Small VSDs Close Spontaneously
- Large VSDs Require Surgery
- Endocarditis
- Eisenmenger's Syndrome
- CHF
Patent Ductus Arteriosus
- Continuous
- Machine like murmur
- Often Due to Congenital Rubella
- Prematurity
Hypertrophic Cardiomyopathy Mechanisms
- 2/3 Autosomal-Dominant
- 1/3 Sporadic Type
- Mutation in Gene for Sarcomere Protein
- Cardiac Myosin Binding Protein C
- Asymmetric Septal Hypertrophy
- Outflow Tract Obstruction
- Diastolic Dysfunction
Total Anomalous Pulmonary Venous Return (TAPVR)
- Pulmonary Veins Do Not Connect to Left Atrium
- Oxygenated Blood Return to Right Atrium
- Incompatible with Life without a Shunt
- Vessel Enters at an Acute Angle
- Severe Cyanosis
- Pulmonary Edema
- Delayed Manifestation (1 or 2 years)
- Right Heart Failure
- Chest X-ray Shows "Snowman"
- Echocardiogram
- Surgical Correction
Hypertrophic Cardiomyopathy Signs, Symptoms and Treatment
- Sudden Death Of Young Athlete
- Heart Failure
- Angina
- Arrhythmias
- Syncope
- Harsh Systolic Ejection Murmur
- S4 Heart Sound
- Beta Blocker
- Non-dihydropyridine Calcium Channel Blocker
Transposition of Great Vessels
- Pulmonary and Systemic Circulation are in Parallel
- Incompatible with Life Without a Shunt
- Severe Cyanosis at Birth
- Single S2 sound
- Echocardiogram
- Chest X-ray shows "Egg-shaped Silhouette"
- Prostaglandin
- Avoid NSAIDs
- Surgical Correction
- Balloon Atrial Septostomy
Kawasaki Disease
- Prevalent in Asian Children
- Necrotizing Vasculitis
- Fever
- Strawberry-Red Tongue and Mucosa
- Lymphadenopathy
- Desquamative Skin Rash
- Erythema and Edema of the Hands and Feet
- Conjunctivitis
- Coronary Aneurysm
- Intravenous Immunoglobulin (IVIG)
- Aspirin
Coarctation of The Aorta
- Constriction of a Portion of Aorta
- Turner Syndrome
- Asymptomatic Hypertension
- BP Higher in Upper Extremities, Right Arm
- CHF
- Echocardiogram
- Cardiac Catheterization
- 3 Sign on Chest X-Ray
- Rib Notching
- Surgical Correction
Rheumatic Fever
- Pharyngeal Infection with Strep Pyogenes (Group A Strep)
- Rheumatic Heart Disease
- Aschoff Bodies
- Anitschkow's Cells
- Early Death Due to Myocarditis
- Migratory Polyarthritis
- Subcutaneous Nodules
- Erythema Marginatum
- Chorea
- Elevated ESR
Brugada Syndrome
- Defective Myocardial Sodium Channels
- Predominance in Asian Males
- Autosomal Dominant
- Pseudo-Right Bundle Branch Block Pattern
- Persistent ST Elevations in Leads V1-V2
- Risk of VTACH and Sudden Cardiac Death
- Syncope
- ICD
- Antiarrhythmics
Congenital Long QT Syndrome
- Inherited Disorder of Myocardial Repolarization
- Potassium (K+) Channel Mutations
- Prolonged QT Interval
- Torsades de Pointes
- Increased Risk of Sudden Cardiac Death (SCD)
- Romano-Ward Syndrome
- Autosomal Dominant
- Pure Cardiac Phenotype (No Deafness)
- Jervell and Lange-Nielsen Syndrome
- Autosomal Recessive
- Sensorineural Deafness
Hyperlipoproteinemia (Type V Dyslipidemia)
- Increased Cholesterol
- Increased VLDL
- Increased Chylomicrons
- Increased Triglycerides
- Increased Risk of Cardiovascular Disease
- Xanthomas
- Acute Pancreatitis
- Lipid Panel
- Lifestyle Changes
- Statins
- Fibrates
Ebstein's Anomaly
- Displacement of Tricuspid Valve Leaflets
- "Atrialization" of the Right Ventricle
- Lithium Exposure In Utero
- Tricuspid Regurgitation
- Right-Sided Heart Failure