Fanconi Syndrome Characteristics
- Resorption Defect in Proximal Tubule
- Hypophosphatemia
- Rickets
- Osteomalacia
- Hypokalemia
- Metabolic Acidosis
- Type 2 Renal Tubular Acidosis
- Treat Underlying Disorder
- Bicarbonate
Fanconi Syndrome Causes
- Cystinosis
- Dent's Disease
- Wilson's Disease
- Oculocerebrorenal (Lowe) Syndrome
- Galactosemia
- Hereditary Fructose Intolerance
- Glycogen Storage Diseases
- Tyrosinemia
- Tenofovir
- Heavy Metals
- Expired Tetracyclines
- Cisplatin
- Gentamycin (Aminoglycosides)
- Valproate Sodium
- Multiple Myeloma
Type 2 Renal Tubular Acidosis
- Proximal Tubule
- Inability To Reabsorb Bicarbonate
- Fanconi Syndrome
- Sporadic Type
- Familial Types
- Autosomal Recessive
- Acetazolamide
- Decreased Urinary pH
- Hypokalemia
- Treat Underlying Disorder
- Alkali Therapy
Renal Tubular Acidosis Type 4
- Aldosterone Resistance
- Decreased Aldosterone Production
- Addison’s Disease (Primary Adrenal Insufficiency)
- Hyporeninism
- Trimethoprim-Sulfamethoxazole
- Potassium Sparing Diuretics
- Hyperkalemia
- Low Urine pH
- Diminished Ammonium (NH4) Urinary Excretion
- Furosemide
- Fludrocortisone
Distal Renal Tubular Acidosis (Type I)
- Distal Tube
- Defect in H+ Secretion
- Increased Urinary pH
- Urinary pH >5.5
- Hypokalemia
- Amphotericin B Toxicity
- Autoimmune Disease
- Lithium
- Obstruction Of The Urinary Tract
- Kidney Stones
- Bicarbonate