Hereditary Spherocytosis Disease
- Northern Europeans
- Autosomal Dominant
- Spectrin/Ankyrin Deficiency
- Spherocyte Formation
- Hemolytic Anemia
- Bilirubin Gallstones
- Jaundice
- Splenomegaly
Hereditary Spherocytosis Diagnosis & Treatment
- Increased MCHC
- Spherocytes
- Normocytic Anemia
- Eosin-5-Maleimide (EMA) Binding Test
- Osmotic Fragility Test
- Glycerol Lysis Test
- Folic Acid
- Splenectomy
Paroxysmal Nocturnal Hemoglobinuria (PNH)
- Defective PIG-A Gene
- Deficiency of DAF (Decay Accelerating Factor CD55)
- Dark Urine in the Morning
- Intravascular Hemolysis
- Thrombosis
- Decreased CD55 and CD59
- RBC Transfusion
- Eculizumab
- Bone Marrow Transplant is Curative